Objective: To improve clinical recognition and provide research diagnostic criteria for three
clinical syndromes associated with frontotemporal lobar degeneration. Methods: Consensus …

… is suggested, moreover, by the high frequency of these behaviours in patients with semantic
dementia, in whom the predominant pathology is temporal rather than frontal Snowden et al, …

Frontotemporal lobar degeneration (FTLD) is the umbrella term encompassing a heterogeneous
group of pathological disorders. With recent discoveries, the FTLDs have been show to …

Clinical and neuropathological descriptions of patients with non-Alzheimer's disease atrophy
of the frontotemporal lobes have emerged chiefly from Lund, Sweden and Manchester, UK. …

A significant proportion of patients with presenile dementia due to primary cerebral atrophy
do not have Alzheimer's disease. One form of non-Alzheimer dementia may be designated …

OBJECTIVE To test predictions that frontotemporal dementia and semantic dementia give
rise to distinct patterns of behavioural change. METHODS An informant based semistructured …

The identification of a hexanucleotide repeat expansion in the C9ORF72 gene as the cause
of chromosome 9-linked frontotemporal dementia and motor neuron disease offers the …

Four patients are described, in whom a profound and rapidly progressive dementia occurred
in association with clinical features of motor neuron disease. The pattern of dementia …

Objectives This study aimed to gain a better understanding of behavioral abnormalities in
Huntington disease (HD) and to develop a method for reliably assessing these changes. …

Objectives– The study aimed to increase understanding of behavioural changes in
frontotemporal dementia (FTD) and identify features that best differentiate FTD from Alzheimer's …