Article Figures & Data
Figures
- fig 1.
Case 1: 9-year-old girl with profound bilateral congenital sensorineural hearing loss.
A, Axial CT scan shows right petrous bone aplasia with absence of inner ear structures. The medial wall of the middle ear is flattened (arrow), being in close contact with the infratentorial nervous structures. Note normal differentiation of the malleus.
B, Coronal CT scan shows a normally developed external and middle right ear. The long process of the incus (arrow) leans against the medial middle ear wall. The oval window, the stapes, and the second portion of the facial nerve are absent. A small dehiscence of the medial wall of the middle ear (arrowhead), located at the IAM, probably corresponds to the entrance of the facial nerve.
- fig 2.
Case 2: 16-year-old boy, brother of girl in case 1, also with profound bilateral congenital sensorineural hearing loss.
A, Axial CT scan shows an aberrant course of the left internal carotid artery, which bulges into the middle ear (white arrow). Dehiscence of the lateral wall of the petrous bone adjacent to the horizontal carotid artery is present (black arrow). A small lateral tract corresponds to a persistent stapediohyoid artery (white arrowhead). The facial nerve passes behind the internal carotid artery (black arrowheads).
B, Coronal CT scan shows enlargement of inferior tympanic canaliculus (arrowhead). Arrow indicates jugular foramen.
