RT Journal Article
SR Electronic
T1 Leptomeningeal Interfoliar Enhancement on Vessel Wall MR Imaging as a Unique Radiologic Finding of Susac Syndrome
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 271
OP 273
DO 10.3174/ajnr.A7801
VO 44
IS 3
A1 P. Cardozo
A1 M. Marrodán
A1 A. Gilmore
A1 M.P. Fiol
A1 H. Chaves
YR 2023
UL http://www.ajnr.org/content/44/3/271.abstract
AB SUMMARY: Susac syndrome is a rare disorder affecting the brain, retina, and inner ear, probably triggered by an immune-mediated endotheliopathy. Diagnosis is based on clinical presentation and ancillary test findings (brain MR imaging, fluorescein angiography, and audiometry). Recently, vessel wall MR imaging has shown increased sensitivity in the detection of subtle signs of parenchymal, leptomeningeal, and vestibulocochlear enhancement. In this report, we describe a unique finding identified using this technique in a series of 6 patients with Susac syndrome and discuss its potential value for diagnostic work-up and follow-up.SuSSusac syndromeVW-MRIvessel wall MR imaging