PT - JOURNAL ARTICLE AU - Chu, Winnie C.W. AU - Lee, Vincent AU - Chan, Yu-leung AU - Shing, Matthew MK AU - Chik, Ki-wai AU - Li, Chi-kong AU - Ma, Kwok-chiu TI - Neurocutaneous Melanomatosis with a Rapidly Deteriorating Course DP - 2003 Feb 01 TA - American Journal of Neuroradiology PG - 287--290 VI - 24 IP - 2 4099 - http://www.ajnr.org/content/24/2/287.short 4100 - http://www.ajnr.org/content/24/2/287.full SO - Am. J. Neuroradiol.2003 Feb 01; 24 AB - Summary: Neurocutaneous melanosis is a rare congenital syndrome characterized by large or multiple congenital melanocytic nevi and benign or malignant pigment cell tumors of the leptomeninges. The prognosis is extremely poor for symptomatic patients, even in the absence of malignant melanoma. We present serial MR imaging findings in the brain and spine of a child with congenital giant hairy nevi who developed progressive leptomeningeal melanomatosis and whose neurologic condition rapidly deteriorated.