RT Journal Article
SR Electronic
T1 X-Linked Stapes Gusher: CT Findings in One Patient
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 1130
OP 1132
VO 24
IS 6
A1 Gaurav Kumar
A1 Mauricio Castillo
A1 Craig A. Buchman
YR 2003
UL http://www.ajnr.org/content/24/6/1130.abstract
AB Summary: A 31-year-old male patient presented with progressive mixed hearing loss since birth. A stapedectomy was attempted and was unsuccessful because of perilymph gushing. CT of the temporal bones showed bulbous dilatation of the fundi of the internal auditory canals and absence of the bone plates separating them from the base of the cochleas. This unusual abnormality was found after the attempted stapedectomy and explains the clinical findings. The findings in male patients are fairly typical X-linked congenital deafness.