PT  - JOURNAL ARTICLE
AU  - Zhang, Wenbo
AU  - Simos, Panagiotis G.
AU  - Ishibashi, Hideaki
AU  - Wheless, James W.
AU  - Castillo, Eduardo M.
AU  - Breier, Joshua I
AU  - Baumgartner, James E.
AU  - Fitzgerald, Michele E.
AU  - Papanicolaou, Andrew C.
TI  - Neuroimaging Features of Epidermal Nevus Syndrome
DP  - 2003 Aug 01
TA  - American Journal of Neuroradiology
PG  - 1468--1470
VI  - 24
IP  - 7
4099  - http://www.ajnr.org/content/24/7/1468.short
4100  - http://www.ajnr.org/content/24/7/1468.full
SO  - Am. J. Neuroradiol.2003 Aug 01; 24
AB  - Summary: Epidermal nevus syndrome is a kind of neurocutaneous syndrome that is associated with epidermal nevus and a variety of congenital CNS disorders. Clinical presentations include seizures, paresis, mental retardation, and developmental delay. We report three cases with MR imaging and magnetoencephalography findings; one patient underwent ictal and interictal single photon emission CT. Both structural and functional imaging studies indicated that the frontal lobes had lesser involvement or were intact. One patient underwent hemispherectomy because of the medically intractable seizure. He remained seizure free with topiramate monotherapy.