RT Journal Article
SR Electronic
T1 Mesectodermal Leiomyosarcoma of the Ciliary Body
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 1765
OP 1768
VO 24
IS 9
A1 Park, Sun-Won
A1 Kim, Hyung-Jin
A1 Chin, Hee-Seung
A1 Tae, Kee-Sun
A1 Han, Jee-Young
YR 2003
UL http://www.ajnr.org/content/24/9/1765.abstract
AB Summary: We report a case of low-grade mesectodermal leiomyosarcoma of the ciliary body, an extremely rare tumor of neural crest origin, occurring in a 12-year-old boy. MR imaging showed a well-marginated, ovoid soft tissue mass at the right temporal ciliary body, accompanied by total retinal detachment. The mass was slightly hyperintense relative to contralateral vitreous on T1-weighted images and markedly hypointense on T2-weighted images and enhanced very well. Initial biopsy of the mass suggested a peripheral nerve sheath tumor. The mass grew rapidly after biopsy, and enucleation was performed. The final diagnosis based on histology and immunohistochemistry was a low-grade mesectodermal leiomyosarcoma. To our knowledge, this is the first reported case of a malignant form of mesectodermal leiomyoma of the ciliary body.