PT  - JOURNAL ARTICLE
AU  - B.Y. Huang
AU  - C. Zdanski
AU  - M. Castillo
TI  - Pediatric Sensorineural Hearing Loss, Part 2: Syndromic and Acquired Causes
AID  - 10.3174/ajnr.A2499
DP  - 2012 Mar 01
TA  - American Journal of Neuroradiology
PG  - 399--406
VI  - 33
IP  - 3
4099  - http://www.ajnr.org/content/33/3/399.short
4100  - http://www.ajnr.org/content/33/3/399.full
SO  - Am. J. Neuroradiol.2012 Mar 01; 33
AB  - SUMMARY: This article is the second in a 2-part series reviewing neuroimaging in childhood SNHL. Previously, we discussed the clinical work-up of children with hearing impairment, the classification of inner ear malformations, and congenital nonsyndromic causes of hearing loss. Here, we review and illustrate the most common syndromic hereditary and acquired causes of childhood SNHL, with an emphasis on entities that demonstrate inner ear abnormalities on cross-sectional imaging. Syndromes discussed include BOR syndrome, CHARGE syndrome, Pendred syndrome, Waardenburg syndrome, and X-linked hearing loss with stapes gusher. We conclude the article with a review of acquired causes of childhood SNHL, including infections, trauma, and neoplasms. BORbranchio-oto-renalCISSconstructive interference in steady stateIACinternal auditory canalNF-2neurofibromatosis type IISCCsemicircular canalSNHLsensorineural hearing lossT1WIT1-weighted imageT2WIT2-weighted image