PT - JOURNAL ARTICLE AU - Hsu, Wendy C. AU - Loevner, Laurie A. AU - Forman, Mark S. AU - Thaler, Erica R. TI - Superficial Siderosis of the CNS Associated with Multiple Cavernous Malformations DP - 1999 Jul 01 TA - American Journal of Neuroradiology PG - 1245--1248 VI - 20 IP - 7 4099 - http://www.ajnr.org/content/20/7/1245.short 4100 - http://www.ajnr.org/content/20/7/1245.full SO - Am. J. Neuroradiol.1999 Jul 01; 20 AB - Summary: Superficial siderosis of the CNS due to chronic, recurrent subarachnoid hemorrhage is an uncommon and potentially debilitating disorder. The classic clinical manifestation is progressive bilateral sensorineural hearing loss (SNHL), although ataxia and pyramidal signs also are observed frequently. Cavernous malformations rarely present with subarachnoid hemorrhage. We describe an unusual case of a young patient who presented with progressive, bilateral SNHL who was found to have superficial CNS siderosis associated with multiple cavernous malformations.