PT  - JOURNAL ARTICLE
AU  - Hill, S C
AU  - Stein, S A
AU  - Dwyer, A
AU  - Altman, J
AU  - Dorwart, R
AU  - Doppman, J
TI  - Cranial CT findings in sclerosteosis.
DP  - 1986 May 01
TA  - American Journal of Neuroradiology
PG  - 505--511
VI  - 7
IP  - 3
4099  - http://www.ajnr.org/content/7/3/505.short
4100  - http://www.ajnr.org/content/7/3/505.full
SO  - Am. J. Neuroradiol.1986 May 01; 7
AB  - Sclerosteosis or Van Buchem's disease is a rare genetic craniotubular hyperostosis that becomes evident in early childhood and is associated with progressive involvement of the skull. The pathologic changes in the cranium noted on CT are described in three cases. Although the disease is incurable, CT is useful to display the morbid anatomy of the cranium before palliative surgery.