RT Journal Article
SR Electronic
T1 Dental and Facial Bone Abnormalities in Pyknodysostosis: CT Findings
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 132
OP 134
VO 28
IS 1
A1 Fleming, K.W.
A1 Barest, G.
A1 Sakai, O.
YR 2007
UL http://www.ajnr.org/content/28/1/132.abstract
AB SUMMARY: Pyknodysostosis is an autosomal-recessive disorder of osteoclast dysfunction causing osteosclerosis, with associated maxillofacial anomalies. Multidetector CT with multiplanar and 3D reconstruction illustrated the pathologic findings in this case. Abnormalities included multiple retained deciduous teeth, unerupted teeth with associated follicles, an irregularly expanded alveolus and body of the mandible, and an obtuse mandibular angle. Volume-rendered imaging better delineated the irregular dentition, with crowding and retention of deciduous teeth.