PT - JOURNAL ARTICLE AU - Lin, D.D.M. AU - Gailloud, P. AU - McCarthy, E.F. AU - Comi, A.M. TI - Oromaxillofacial Osseous Abnormality in Sturge-Weber Syndrome: Case Report and Review of the Literature DP - 2006 Feb 01 TA - American Journal of Neuroradiology PG - 274--277 VI - 27 IP - 2 4099 - http://www.ajnr.org/content/27/2/274.short 4100 - http://www.ajnr.org/content/27/2/274.full SO - Am. J. Neuroradiol.2006 Feb 01; 27 AB - SUMMARY: We report a case of a 17-month-old child affected by Sturge-Weber syndrome who had unusually rapid overgrowth of the left frontal, temporal, orbital, and maxillary regions. CT angiography illustrated osteohypertrophy with periostitis and associated soft tissue hypertrophy directly corresponding to the distribution of the cutaneous port-wine stain. Extended maxillectomy was performed because of rapid growth and clinical debilitation, with surgical pathology revealing juvenile ossifying fibroma.