PT  - JOURNAL ARTICLE
AU  - Koyama, M.
AU  - Yagishita, A.
TI  - Pantothenate Kinase-Associated Neurodegeneration with Increased Lentiform Nuclei Cerebral Blood Flow
DP  - 2006 Jan 01
TA  - American Journal of Neuroradiology
PG  - 212--213
VI  - 27
IP  - 1
4099  - http://www.ajnr.org/content/27/1/212.short
4100  - http://www.ajnr.org/content/27/1/212.full
SO  - Am. J. Neuroradiol.2006 Jan 01; 27
AB  - Summary: We report a case of pantothenate kinase-associated neurodegeneration with increased regional cerebral blood flow (rCBF) in bilateral lentiform nuclei on technetium Tc-99m ethyl cysteinate dimer single-photon emission CT (ECD-SPECT). A 6-year-old boy presented with opisthotonus. T2*-weighted MR images revealed areas of marked hypointensity with a hyperintense focus in bilateral globus pallidus, creating the characteristic eye-of-the-tiger appearance. ECD-SPECT showed increased rCBF in bilateral lentiform nuclei.