RT Journal Article SR Electronic T1 Serial MR Imaging, Diffusion Tensor Imaging, and MR Spectroscopic Findings in a Child with Progressive Encephalopathy, Edema, Hypsarrhythmia, and Optic Atrophy (PEHO) Syndrome JF American Journal of Neuroradiology JO Am. J. Neuroradiol. FD American Society of Neuroradiology SP 1555 OP 1558 VO 27 IS 7 A1 Huisman, T.A.G.M. A1 Klein, A. A1 Werner, B. A1 Straube, T. A1 Boltshauser, E. YR 2006 UL http://www.ajnr.org/content/27/7/1555.abstract AB SUMMARY: PEHO syndrome is a rare symptom complex of severe progressive encephalopathy, edema, hypsarrhythmia, and optic atrophy. Disease onset is in early infancy. The current case report presents and discusses serial conventional MR imaging findings and serial functional studies including diffusion tensor imaging and quantitative MR spectroscopy findings in a 6-year-old child with PEHO.