TY - JOUR T1 - Pulsatility Attenuation along the Carotid Siphon in Pseudoxanthoma Elasticum JF - American Journal of Neuroradiology JO - Am. J. Neuroradiol. SP - 2030 LP - 2033 DO - 10.3174/ajnr.A7288 VL - 42 IS - 11 AU - J.W. Bartstra AU - R.J. van Tuijl AU - P.A. de Jong AU - W.P.T.M. Mali AU - I.C. van der Schaaf AU - Y.M. Ruigrok AU - G.J.E. Rinkel AU - B.K. Velthuis AU - W. Spiering AU - J.J.M. Zwanenburg Y1 - 2021/11/01 UR - http://www.ajnr.org/content/42/11/2030.abstract N2 - SUMMARY: We compared velocity pulsatility, distensibility, and pulsatility attenuation along the intracranial ICA and MCA between 50 patients with pseudoxanthoma elasticum and 40 controls. Patients with pseudoxanthoma elasticum had higher pulsatility and lower distensibility at all measured locations, except for a similar distensibility at C4. The pulsatility attenuation over the siphon was similar between patients with pseudoxanthoma elasticum and controls. This finding suggests that other disease mechanisms are the main contributors to increased intracranial pulsatility in pseudoxanthoma elasticum.PIpulsatility indexPXEpseudoxanthoma elasticumSVDsmall-vessel disease2D-PC2D phase-contrast ER -