Case No. | Age at Onset (yr) | Sex | Duration (yr) | Rigidity | Dystonia | Pyramidal Signs | Cortical Dysfunction | Vertical Gaze Palsy | Dementia | CDx |
---|---|---|---|---|---|---|---|---|---|---|
1 | 74 | F | 10 | Lt>Rt | – | – | Ocular apraxia | + | Mute | PSP? |
2 | 68 | F | 6 | Lt>Rt | Apraxia (Lt hand) | ± | + Severe akinetic mute | AD | ||
3 | 67 | M | 3 | Rt>Lt | No cortical sign | + | + Severe | PDD | ||
4 | 74 | F | 6 | Rt>Lt | – | – | – | + | + Severe | CBD |
Note:—CBD indicates corticobasal degeneration; PSP?, progressive supranuclear palsy suspected; CDx, clinical diagnosis; AD, Alzheimer disease; PDD, Parkinson disease with dementia; –, no symptom; +, obvious symptom; ±, suspicious symptom; Lt, left; Rt, right.