Table 1:

Brain MR imaging scoring system for MLD

Brain Areas	Score^*			Maximum per Area
Frontal WM	6^†
Periventricular	0	1	2
Central	0	1	2
U-fibers	0	1	2
Parieto-occipital WM	6^†
Periventricular	0	1	2
Central	0	1	2
U-fibers	0	1	2
Temporal WM	6^†
Periventricular	0	1	2
Central	0	1	2
U-fibers	0	1	2
Corpus callosum	4^†
Genu	0	1	2
Splenium	0	1	2
Projection fibers	6^†
Internal capsule posterior limb	0	1	2
Internal capsule anterior limb	0	1	2
Midline pons	0	1	2
Cerebral atrophy	0	1	2	2^†
Thalamus	0	1		1^†
Basal ganglia	0	1	1^†
Cerebellum	2^†
WM	0	1
Atrophy	0	1
Total				34^†