Clinical and MR imaging findings in PMG patients

PatientAgeSexClinical ManifestationOther MR FindingsPMG LocationEvaluated LesionT1 PatternThickness (mm) Axial (Coronal)T2 PatternThickness (mm) Axial (Coronal)Layer between Cortex and White Matter
13DFZellweger syndromeGerminolytic cystsbil. SylSyl24 (4)14
22MMEpilepsybil. F, Syr, PSyl24 (3)14 (3)
33MFInfantile spasmusMicrocephaly, hypoplastic CCbil. Syl, PSylUndifferentiated13 (4)
43MMLarge head, retardationrt. hemiP25 (5)14
7MP26 (6)14
11MP2614Present
2YF2513Present
P2626
55MMRetardationbil. TTUndifferentiated13
67MMInfantile spasmusdiffuseSyl2613 (3)
712MFIn utero drug exposurelt. F, SylSyl27 (6)14
815MFrt. hemiparesislt. F, P, bil. SyrF26 (5)13Present
P26 (6)26
915MMlt. hemiparesisrt. hemiF27 (7)14Present
P27 (6)27
1018MFRetardation, focal seizuresmall rt. Th, peduclert. hemiF26 (6)13Present
P26 (6)26
1118MMSeizureheterotopiabil. Syl, PSyr26 (6)26
123YMrt. hemiparesislt. hemiSyr27 (6)27
138YMSpeech delayrt. hemi, lt. FIns28 (8)28
148YMHydrocephalusheterotopia, Agenesis of CCbil. FF26 (6)26
159YFRetardationheterotopia, hypoplastic CCbil. FF28 (7)28
1611YMRetardationheterotopia, agenesis of CClt. FF27 (6)27
1743YFEpilepsybil. SyrSyr26 (6)26
  • Note.—PMG, polymicrogyria; D, day; M, month; Y, year; CC, corpus callosum; Th, thalamus; bil, bilateral; rt, right; lt, left; F, frontal; Syl, Sylvian; P, parietal; hemi, hemispheric.