Imaging features of X-linked congenital mixed deafness (findings bilateral in all patients)

AuthorsTotal Number of Patients/GenderEnlarged IACaAbsent/Hypoplastic Bony Plate at Fundus of IACAbsent ModiolusAbnormal Vestibular AqueductWide Facial Nerve Canals
Phelps et al (3)24/male1616Not describedNot described16
Talbot and Wilson (4)4/male34444
Tang and Parnes (5)2/male222Not described1
Papadaki et al (6)2/female22Not describedNot described2
  • a IAC, internal auditory canals.