Classification of MRI findings according to severity

Malformation TypeSeverity
Normal VariantMinor FindingsMajor Findings
NTDMeningoceleAcrania/anencephaly encephalocele
Myelocele
Cystic lesionsCPCIsolated PVPCNonisolated PVPC
Cavum vergeArachnoid cystPVL
CVIPorencephalic cyst
BleedingIVH grade 1IVH grade 2–4
IschemiaParenchymatic damage
Cortical disordersDelayed sulcation (up to 2 weeks)Lissencephaly
Schizencephaly
Heterotopia
Microcephaly
White matterIsolated T2 hypersignalNonisolated T2 hypersignal
Midline CCLipomaShort intact CC thick/thinComplete/partial CC agenesis
Midline CSPIsolated septal agenesisSOD
Posterior fossaMCMBlake pouch cystChiari 2
DWS
Primary disruption of cerebellum/vermis/brain stem
Secondary disruption of cerebellum/vermis/brain stem
VascularVein of Galen aneurysm
  • Note:—NTD indicates neural tube defect; CPC, choroid plexus cyst; CVI, cavum vellum interpositum; PVPC, periventricular pseudocyst; PVL, periventricular leukomalacia; IVH, intraventricular hemorrhage; CMV, cytomegalovirus; CC, corpus callosum; CSP, cavum septum pellucidum; SOD, septo-optic dysplasia; MCM, mega cysterna magna; DWS, Dandy-Walker syndrome; CSVT, cerebral sinovenous thrombosis.