Table 2:

Arterial components around the distal ICA on the affected side in patients with and without PHACE syndromea

PHACE (+) (n = 11)PHACE (−) (n = 9)P Valueb
A1Dysplasia = 8 (72.7%)Dysplasia = 7 (77.8%)1.000
M1Dysplasia = 0 (0.0%)Dysplasia = 2 (22.2%).189
OAEctopic = 1 (9.1%)Ectopic = 4 (44.4%).127
AchoADysplasia = 3 (27.3%)Dysplasia = 2 (22.2%)1.000
PcomADysplasia = 7 (63.6%)Dysplasia = 7 (77.8%).642
MidbrainDysplasia = 5 (45.5%)Dysplasia = 4 (44.4%)1.000
  • a PHACE includes cases of confirmed and possible PHACE syndrome; a small midbrain was not used as a criterion.

  • b Fisher exact test.