Table 1:

Demographic and clinical characteristics of patients with CTD

CharacteristicCTD (N = 68)Marfan Syndrome (n = 36)LDS (n = 32)P
Age at MRA, median (IQR), y38.5 (23–48)32.5 (25–43.5)42 (22–50).21
Female, n (%)33 (48.5)15 (41.7)18 (56.3).33
Aortic root dilation, n (%)59 (86.8)33 (91.7)26 (81.3).29
Aortic dissection, n (%)9 (13.2)6 (16.7)3 (9.4).48
Arterial dissection, n (%)4 (5.9)0 (0.0)4 (12.5).04
Aortic surgery, n (%)41 (60.3)25 (69.4)16 (50.0).14
Age at surgery, median (IQR), y28 (20–37)26 (21–35)33 (18–44).47