Table 1:

The demographic and clinical characteristics in patients with Wolfram syndrome at first and last follow-up visitsa

First Visit (n = 30)Last Visit (n = 30)
Age (yr)14 ± 619 ± 6
Duration of disease (yr)3 ± 38 ± 4
Diabetes mellitus29 (97) 30 (100)
Vision impairment28 (93) 28 (93)
Hearing loss 20 (67)23 (77)
Diabetes insipidus15 (50)19 (63)
Bladder dysfunction13 (43)26 (86)
  • a For the age and duration of disease, means and SDs are reported. For comorbid conditions, numbers and percentages are reported.