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Aneurysms of the vein of Galen in infants aged 2 to 15 months. Diagnosis and natural evolution

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Summary

This is a report of seven cases of aneurysm of the vein of Galen (AVG) with a review of the clinical and radiological aspects of 48 cases in the literature. The natural evolution and pathophysiology of this vascular malformation are discussed. The clinical signs of this condition are often misleading. The appearance of AVG on CT is pathognomic. Surveillance of the vascular malformation and associated cerebral lesions can be maintained with subsequent CT. Spontaneous thrombosis of the aneurysm was observed in three cases. The diagnosis of thrombosis of the AVG was always made at operation or by histological examination. The radiological appearance of a thrombosed aneurysm is typical.

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Authors and Affiliations

  1. Service de Radiologie, Hôpital des Enfants Malades, Paris, France

    C. Diebler & C. Ernest

  2. Unité de Neuroradiologie, Hôpital Foch, Suresnes, France

    C. Diebler

  3. Service de Neuroradiologie, Hôpital Lariboisière, Paris, France

    C. Diebler

  4. Service de Neuropédiatrie, Hôpital Saint Vincent de Paul, Paris, France

    O. Dulac

  5. Service de Neurochirurgie, Hôpital des Enfants Malades, Paris, France

    Dominique Renier

  6. Service de Radiologie, Hôpital Saint Vincent de Paul, Paris, France

    G. Lalande

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  1. C. Diebler
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  2. O. Dulac
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  3. Dominique Renier
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  4. C. Ernest
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  5. G. Lalande
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Diebler, C., Dulac, O., Renier, D. et al. Aneurysms of the vein of Galen in infants aged 2 to 15 months. Diagnosis and natural evolution. Neuroradiology 21, 185–197 (1981). https://doi.org/10.1007/BF00367340

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  • DOI: https://doi.org/10.1007/BF00367340

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