Summary
The MR findings in an adult patient with globoid cell leucodystrophy (GLD) or Krabbe's disease are presented. MRI showed a bilateral periventricular hyperintensity of the parieto-occipital white matter on the T2-weighted images. A hyperintense signal was seen bilaterally along the corticospinal tract. There was no immediate nor delayed contrast enhancement. The MR findings in this case of GLD are rather atypical.
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Demaerel, P., Wilms, G., Verdru, P. et al. MR findings in globoid cell leucodystrophy. Neuroradiology 32, 520–522 (1990). https://doi.org/10.1007/BF02426470
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DOI: https://doi.org/10.1007/BF02426470