Abstract
Background
Juvenile xanthogranuloma (JXG) is a disorder of histiocyte proliferation. Most cases present with a solitary cutaneous lesion. JXG with systemic involvement is rare with significant morbidity. Intracranial solitary JXG may be misdiagnosed before operation.
Methods
A 5-month-old boy showed an elevated anterior fontanel but no other abnormalities on admission. Brain MRI showed a large mass in the right parietal region.
Results
The tumor was removed with the encroached meninges. A JXG in the right parietal region was diagnosed pathologically.
Conclusion
Total excision of the tumor may be curative with a prerequisite of ensuring normal vital signs and nervous function.
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Sun, LP., Jin, HM., Yang, B. et al. Intracranial solitary juvenile xanthogranuloma in an infant. World J Pediatr 5, 71–73 (2009). https://doi.org/10.1007/s12519-009-0015-4
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DOI: https://doi.org/10.1007/s12519-009-0015-4