Research paper
Acute mastoiditis complicated by sigmoid sinus thrombosis in congenital aural atresia

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Abstract

Congenital aural atresia occurs approximately once in every 20,000 live births, although the incidence of otitis media in aural atretic children should not differ from the rest of the population, detection is difficult. Unless severe, the infection usually goes unnoticed, especially with the use of antibiotics. A two-year-old male with congenital aural atresia presented with fever and facial nerve paresis. As his illness progressed, he developed mastoiditis with subperiosteal abscess and sigmoid sinus thrombosis. Literature review showed this to be the first reported case of sigmoid sinus thrombosis in congenital aural atresia. Diagnosis and management are presented.

References (28)

  • L.G. Close et al.

    Coalescent mastoiditis in a case of congenital aural atresia

    Int. J. Pediatr. Otorhinolaryngol.

    (1982)
  • F. Tovi et al.

    Silent mastoiditis and bilateral simultaneous facial palsy

    Int. J. Pediatr. Otorhinolaryngol.

    (1983)
  • F.R. Venezio et al.

    Complications of mastoiditis with special emphasis on venous sinus thrombosis

    Pediatrics

    (1982)
  • F. Altmann

    Congenital atresia of the ear in man and animals

    Ann. Otol. Rhinol. Laryngol.

    (1955)
  • F. Altran

    Missbildungen des Ohres

  • J.W. Ballantyne

    The teratologial records of Chaldea

    Teratologia

    (1894)
  • R.J. Belluci

    The problem of congenital auricular malformations. I. Construction of the external auditory canal

    Trans Am. Acad. Ophthalmol. Otolaryngol.

    (1960)
  • C.B. Courville

    Intracranial complications of otitis media and mastoiditis in the antibiotic era

    Laryngoscope

    (1953)
  • J.S. Fraser

    Maldevelopments of the aurile, external acoustic meatus and middle ear

    Arch. Otolaryngol.

    (1931)
  • N.W. Gill

    Congenital atresia of the ear: a review of the surgical findings in 83 cases

    J. Laryngol. Otol.

    (1969)
  • N.W. Gill

    Congenital atresia of the ear

    J. Laryngol. Otol.

    (1971)
  • C.M. Ginsburg et al.

    Acute mastoiditis in infants and children

    Clin. Pediat.

    (1980)
  • D.B. Hawkins et al.

    Acute mastoiditis in children: a review of 54 cases

    Laryngoscope

    (1983)
  • B.E. Hoenk et al.

    Chole steatoma auris behind a bony atresia plate

    Arch. Otolaryngol.

    (1969)
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