Double-Lumen Aortic Arch: Persistence of the Fifth Aortic Arch

Phillip S Naimo; Maria Del Carmen Vazquez-Alvarez; Yves d'Udekem; Bryn Jones; Igor E Konstantinov

doi:10.1016/j.athoracsur.2015.10.014

Double-Lumen Aortic Arch: Persistence of the Fifth Aortic Arch

Ann Thorac Surg. 2016 May;101(5):e155-6. doi: 10.1016/j.athoracsur.2015.10.014.

Authors

Phillip S Naimo¹, Maria Del Carmen Vazquez-Alvarez², Yves d'Udekem¹, Bryn Jones¹, Igor E Konstantinov³

Affiliations

¹ Royal Children's Hospital, Melbourne, Australia; Murdoch Children's Research Institute, Melbourne, Australia; University of Melbourne, Melbourne, Australia.
² Royal Children's Hospital, Melbourne, Australia; Murdoch Children's Research Institute, Melbourne, Australia.
³ Royal Children's Hospital, Melbourne, Australia; Murdoch Children's Research Institute, Melbourne, Australia; University of Melbourne, Melbourne, Australia. Electronic address: igor.konstantinov@rch.org.au.

PMID: 27106464
DOI: 10.1016/j.athoracsur.2015.10.014

Abstract

A persistent fifth aortic arch is exceptionally rare. We report a patient with a double-lumen aortic arch in association with a perimembranous ventricular septal defect and Cornelia de Lange syndrome. We also discuss the morphologic consequences of persistent fifth aortic, arch, which may not be limited to the double-lumen aorta but in fact may be more common.

Publication types

Case Reports

MeSH terms

Aorta, Thoracic / abnormalities*
Aorta, Thoracic / pathology
De Lange Syndrome / complications*
Female
Heart Septal Defects, Ventricular / complications*
Humans
Infant