Spectrum of third window abnormalities: semicircular canal dehiscence and beyond

ML Ho, G Moonis, CF Halpin… - American Journal of …, 2017 - Am Soc Neuroradiology
Third window abnormalities are defects in the integrity of the bony structure of the inner ear,
classically producing sound-/pressure-induced vertigo (Tullio and Hennebert signs) and/or a …

[HTML][HTML] Inner-ear disorders presenting with air–bone gaps: a review

A Scarpa, M Ralli, C Cassandro… - The journal of …, 2020 - ncbi.nlm.nih.gov
Air–bone gaps (ABGs) are commonly found in patients with conductive or mixed hearing
loss generally due to outer-and/or middle-ear diseases such as otitis externa, tympanic …

Pediatric sensorineural hearing loss, part 2: syndromic and acquired causes

BY Huang, C Zdanski… - American journal of …, 2012 - Am Soc Neuroradiology
This article is the second in a 2-part series reviewing neuroimaging in childhood SNHL.
Previously, we discussed the clinical work-up of children with hearing impairment, the …

HRCT and MRI findings in X-linked non-syndromic deafness patients with a POU3F4 mutation

WX Gong, RZ Gong, B Zhao - International journal of pediatric …, 2014 - Elsevier
Objective The aim of this study was to analyze HRCT and MRI findings in patients with X-
linked non-syndromic deafness and a POU3f4 mutation. Methods HRCT and MRI data of …

Third window lesions

ML Ho - Neuroimaging Clinics, 2019 - neuroimaging.theclinics.com
Third window abnormalities are bony defects of the inner ear that enable abnormal
communication with the middle ear and/or cranial cavity. Normally, the inner ear and middle …

Management of conductive hearing loss in children

W Dougherty, BW Kesser - Otolaryngologic Clinics of North …, 2015 - oto.theclinics.com
While sensorineural hearing loss (SNHL) is far more common in adults, CHL accounts for
90% to 95% of all childhood hearing loss, with middle ear effusion (MEE)/otitis media with …

[HTML][HTML] Novel and De Novo Mutations Extend Association of POU3F4 with Distinct Clinical and Radiological Phenotype of Hearing Loss

A Pollak, U Lechowicz, A Kędra, P Stawiński… - PloS one, 2016 - journals.plos.org
POU3F4 mutations (DFNX2) are the most prevalent among non-syndromic X-linked hearing
loss (HL) identified to date. Clinical manifestations of DFNX2 usually comprise congenital …

[PDF][PDF] Radiological imaging findings of patients with congenital totally hearing loss.

M Dağkıran, N Dağkıran… - Journal of …, 2016 - pdfs.semanticscholar.org
OBJECTIVE: The aim of this study was to determine and classify inner ear abnormalities in
patients who had cochlear implants because of congenital sensorineural hearing loss using …

Temporal bone and intracranial abnormalities in syndromic causes of hearing loss: an updated guide

F D'Arco, A Youssef, E Ioannidou, S Bisdas… - European Journal of …, 2020 - Elsevier
Purpose To describe in detail the temporal bone and brain findings in both common and
rare syndromic causes of hearing loss, with the purpose of broadening among radiologists …

[HTML][HTML] Audiovestibular quantification in rare third window disorders in children

S Dasgupta, S Ratnayake, R Crunkhorn, J Iqbal… - Frontiers in …, 2020 - frontiersin.org
Third window disorders are structural abnormalities in the bony otic capsule that establish a
connection between the middle/inner ear or the inner ear/cranial cavity. Investigated …