In the multidisciplinary management of patients with inner ear malformations (IEMs), the
correct diagnosis makes the differences in terms of clinical and surgical treatment. The …

Moderate-to-profound sensorineural hearing loss in humans is treatable by electrically
stimulating the auditory nerve (AN) with a cochlear implant (CI). In the cochlea, the modiolus …

Conductive hearing losses are typically present in disorders of the external/middle ear.
However, there is a rare group of inner ear conditions called third windows that can also …

The incomplete partition type III is a severe cochlear malformation present in X-linked
deafness. It is a rare, non-syndromic cause of severe to profound mixed hearing loss, often …

PURPOSE X-linked deafness (XLD) is a rare disease characterized by typical cochlear
incomplete partition type 3 (IP-III) anomaly. Accompanying hypothalamic anomalies were …

Objective Preoperative assessment of the cochlear duct length (CDL) and cochlear
dimensions allows the selection of optimized implants. We aimed to evaluate the CDL …

Mutations and deletions in the gene or upstream of the gene encoding the POU3F4
transcription factor cause X‐linked progressive deafness DFNX2 and additional …

Conductive hearing losses are typically present in disorders of the external/middle ear.
However, there is a rare group of inner ear conditions called third windows that can also …

Although the technical challenge has increased, along with the complexity of accessing the
cochlea and electrode array insertion following the introduction of cochlear implant surgery …

Congenital malformations are the most common cause of hearing loss in children and the
most common cause of temporal bone imaging in childhood. In the vast majority of cases …