Objective: To improve clinical recognition and provide research diagnostic criteria for three
clinical syndromes associated with frontotemporal lobar degeneration. Methods: Consensus …

The identification of a hexanucleotide repeat expansion in the C9ORF72 gene as the cause
of chromosome 9-linked frontotemporal dementia and motor neuron disease offers the …

The chromosome 9p21 amyotrophic lateral sclerosis-frontotemporal dementia (ALS-FTD)
locus contains one of the last major unidentified autosomal-dominant genes underlying these …

Thirteen families have been described with an autosomal dominantly inherited dementia
named frontotemporal dementia and parkinsonism linked to chromosome 17 (FTDP-17) 1 , 2 , 3 …

Frontotemporal dementia (FTD) is the second most common cause of dementia in people
under the age of 65 years 1 . A large proportion of FTD patients (35–50%) have a family history …

Presents case reports of a 67-yr-old man and 2 women (aged 60 and 66 yrs) with primary
cerebral atrophy in whom progressive breakdown in language and visual perception are …

Frontotemporal dementia (FTD) is a focal clinical syndrome characterised by profound changes
in personality and social conduct and associated with circumscribed degeneration of the …

This article presents the revised consensus criteria for the diagnosis of frontotemporal
dysfunction in amyotrophic lateral sclerosis (ALS) based on an international research workshop …

BackgroundFrontotemporal dementia accounts for up to 20% of cases of dementia in the
presenium, yet remains poorly recognised. Diagnostic criteria have been devised to aid clinical …

Objectives This study aimed to gain a better understanding of behavioral abnormalities in
Huntington disease (HD) and to develop a method for reliably assessing these changes. …