Primary CNS vasculitis is an uncommon disorder of unknown cause that is restricted to brain
and spinal cord. The median age of onset is 50 years. The neurological manifestations are …

Objective A novel autoimmune central nervous system (CNS) disorder with glial fibrillary
acidic protein (GFAP)‐IgG as biomarker was recently characterized. Here, 102 patients with …

Vasculitis is inflammation of the blood vessels, which may involve either the central nervous
system (CNS), or the peripheral nervous system (PNS), or both. This involvement may be …

BACKGROUND AND PURPOSE: Primary angiitis of the central nervous system of childhood
(cPACNS) is a rare and ill-defined disease. In the absence of a brain biopsy, the diagnosis is …

Primary central nervous system vasculitis (PCNSV) is a rare and poorly understood
syndrome. We describe the clinical findings in 8 patients who appear to have a distinct …

BACKGROUND AND PURPOSE: Clinical diagnosis of lymphomatoid granulomatosis (LG)
of the brain, in patients without skin or chest lesions, usually is difficult because of the …

A vasculitis of small arteries and veins of unknown cause restricted to the central nervous
system (CNS) was initially described from autopsy material as granulomatous angiitis of the …

Both the central nervous system (CNS) and the peripheral nervous system (PNS) are major
target organs in primary vasculitides. They may either be affected in the setting of systemic …

Purpose: MR imaging and cerebral angiography were correlated in patients with primary
angiitis of the central nervous system (PACNS) to assess the relative roles of these imaging …

We present a case of multifocal enhancing lesions confined to the right cerebral hemisphere
that mimicked diffuse neoplasm. MR spectroscopy revealed not only minimal elevation of the …