Sturge-Weber Disease with Repercussion on the Prenatal Development of the Cerebral Hemisphere

MR images in a patient with SWD.

A, Axial inversion-recovery T1-weighted image obtained when the patient was aged 3 months shows a decrease in the size of the left hemisphere in the parietal region and a pachygyric appearance of the cortex.

B, Coronal T2-weighted image shows a pachygyric pattern in the left cortex, with irregularities in the cortical-white matter junctions.

C, Coronal T2-weighted image obtained after the injection of gadolinium-based contrast agent when the patient was aged 20 months shows an enlarged left choroid plexus, enhancement of the pial angioma, and large subarachnoid spaces on the left side without noticeable ventricular dilatation.